Abstract
The perianesthetic care of the child with a metabolic disorder is a stressful experience for the child’s family and at least a pharmacologic challenge for the anesthesiologist. A careful team approach is necessary to plan each aspect of anesthetic care. Moreover, mild forms of metabolic disorders can present as unexplained perioperative events: the anesthesiologist should keep the diagnosis of previous undiagnosed metabolic disorder in its diagnostic approach to these problems. This chapter proposes a frame to help the anesthesiologist establishing an anesthetic plan adapted to the child’s known or suspected pathology and its current preoperative status and highlights the importance of developing a “metabolic reflex” when a child presents with an unusual clinical picture in the perioperative period.
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Francis, V., Jean-Louis, S. (2016). Perioperative Care of Children with a Metabolic Disease. In: Astuto, M., Ingelmo, P. (eds) Perioperative Medicine in Pediatric Anesthesia. Anesthesia, Intensive Care and Pain in Neonates and Children. Springer, Cham. https://doi.org/10.1007/978-3-319-21960-8_13
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DOI: https://doi.org/10.1007/978-3-319-21960-8_13
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