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Juvenile X-Linked Retinoschisis

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Manual of Retinal Diseases


Juvenile X-linked retinoschisis is a hereditary disorder characterized by foveal schisis affecting males early in life. Schisis or splitting of the retina’s neurosensory layers in the periphery can also be seen in some cases.

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  1. 1.

    Mizuo-Nakamura phenomenon is a change in the color of the fundus from red in the dark-adapted state to golden immediately or shortly after exposure to light. The color of the fundus reflex can be either homogeneous or streaky.

References and Suggested Reading

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Correspondence to Norberto Mancera MD .

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Mancera, N., Bhaleeya, S. (2016). Juvenile X-Linked Retinoschisis. In: Medina, C., Townsend, J., Singh, A. (eds) Manual of Retinal Diseases. Springer, Cham.

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-20459-8

  • Online ISBN: 978-3-319-20460-4

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