Abstract
Left ventricular non-compaction (LVNC) is a rare congenital cardiomyopathy characterized by a “spongy” feature of the myocardium. The main clinical manifestations are heart failure, supraventricular or ventricular arrhythmias, and thromboembolic events. They can appear simultaneously or separately. We reported the clinical case of a 50-year-old man referred to the family doctor for worsening dyspnea and fatigue during ordinary physical activities and 2 syncope preceded by dyspnea and dizziness. The patient was then referred to our cardiology department for further evaluation, and a severe dysfunction of the left ventricle was revealed with myocardial non-compaction pattern of the apex and side wall visible in echocardiography and cardiac MR. The patient underwent intravenous diuretic therapy with improvement of symptoms, and during the hospitalization, a non-sustained ventricular tachycardia was recorded. Considering ventricular tachycardia as the most probable cause of the syncope referred from the patient and the high arrhythmic risk of non-compaction cardiomyopathy, the patient underwent implantation of a two-chamber ICD. Medical therapy for heart failure was administered too.
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Maolo, A., Masiero, S. (2015). Left Ventricular Non-compaction Cardiomyopathy. In: Capucci, A. (eds) Clinical Cases in Cardiology. Springer, Cham. https://doi.org/10.1007/978-3-319-19926-9_13
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DOI: https://doi.org/10.1007/978-3-319-19926-9_13
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