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Tibial Hemimelia

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Pediatric Lower Limb Deformities

Abstract

Tibial hemimelia is a rare congenital deficiency that involves a spectrum of deformity of the tibia, ranging from mild shortening to total absence of the tibia. This chapter is a comprehensive review of the management principles of children born with tibial hemimelia as well as the senior author’s experience with the treatment of multiple types. The genetics, etiology, and anatomy of tibial hemimelia are described, followed by a review of various classification schemes. A detailed history of treatment for tibial hemimelia and their published results are discussed. New treatment strategies for limb reconstruction are discussed with advanced surgical techniques based on the Paley classification scheme. Techniques include the author’s modification of Brown’s centralization of the fibula and Weber’s patellar arthroplasty, as well as the use of multiplanar external fixators for correction of deformity, soft tissue distraction, and lengthening for limb salvage reconstruction.

An erratum to this chapter can be found at DOI 10.1007/978-3-319-17097-8_33

An erratum to this chapter can be found at http://dx.doi.org/10.1007/978-3-319-17097-8_33

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Authors and Affiliations

  1. St. Mary’s Medical Center, Paley Advanced Limb Lengthening Institute, 901 45th St. , Kimmel Building, West Palm Beach, FL, 33407, USA

    Dror Paley MD, FRCSC

  2. Department of Orthopedic Surgery, University of Oklahoma Health Sciences Center, 940 NE 13th St, Suite 2009/MRI 2000, Oklahoma City, OK, 73104, USA

    David Y. Chong MD

Authors
  1. Dror Paley MD, FRCSC
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  2. David Y. Chong MD
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Correspondence to Dror Paley MD, FRCSC .

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Editors and Affiliations

  1. Professor, Department of Orthopedics; Chief, Division of Pediatric Orthopedics, Rutgers-New Jersey Medical School, Newark, New Jersey, USA

    Sanjeev Sabharwal

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Paley, D., Chong, D.Y. (2016). Tibial Hemimelia. In: Sabharwal, S. (eds) Pediatric Lower Limb Deformities. Springer, Cham. https://doi.org/10.1007/978-3-319-17097-8_24

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  • DOI: https://doi.org/10.1007/978-3-319-17097-8_24

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-17096-1

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