Nutrition for Pancreatic Sufficient Individuals with Cystic Fibrosis

  • John F. PohlEmail author
  • Catherine M. McDonald
Part of the Nutrition and Health book series (NH)


Cystic fibrosis (CF) is typically associated with exocrine pancreatic insufficiency (PI) and nutritional care of the CF patient with exocrine pancreatic sufficiency (PS) is less well described. Although patients with CF and PS typically have milder CF transmembrane conductance regulator (CFTR) gene mutations, they are still at risk of malnutrition without careful monitoring. Tests for pancreatic exocrine status should be used to determine exocrine status as well as to monitor for progression to a PI status. Such tests include the fecal elastase-1 (FE-1) immunosorbent assay which is associated with excellent sensitivity and specificity. Clinicians also should be aware that CF patients with PS are at risk of pancreatitis and testing for this scenario should be considered if clinically warranted.


Pancreas Sufficiency Elastase Celiac Pancreatitis 


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Copyright information

© Springer International Publishing Switzerland 2015

Authors and Affiliations

  1. 1.Division of Pediatric Gastroenterology, Department of Pediatrics, Primary Children’s HospitalUniversity of UtahSalt Lake CityUSA

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