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Nutrition in Cystic Fibrosis pp 207–217Cite as

Nutrition Pre and Post Lung Transplant

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Part of the book series: Nutrition and Health ((NH))

Abstract

Approximately 2800 people with cystic fibrosis (CF) have received a lung transplant since 1990; CF is the third major indication for lung transplantation after emphysema and pulmonary fibrosis. Malnutrition is a common finding in CF patients prior to transplant, and those with a BMI < 18.5, and/or a depletion of fat free mass, and/or serum albumin <3 mg/dl are at higher risk for negative post-transplant outcomes.

Tube feedings may be effective in stabilizing or improving nutritional status prior to transplantation; however, it is important to be aware of potential complications and specific needs such as enzyme replacement associated with tube feeding in individuals with CF.

Nutritional status generally improves post-transplant despite various complications that can affect the gastrointestinal tract and oral intake. CF patients should continue to be monitored by their CF team alongside the transplant team after transplant to help manage the remaining GI and endocrine aspects of CF.

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Author information

Authors and Affiliations

  1. Pediatric Pulmonology, Rainbow Babies and Children’s Hospital Case Medical Center, 11100 Euclid Ave, Cleveland, OH, 44106, USA

    Teresa Schindler M.S., R.D.N.

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  1. Teresa Schindler M.S., R.D.N.
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Correspondence to Teresa Schindler M.S., R.D.N. .

Editor information

Editors and Affiliations

  1. Department of Pediatrics, Division of Gastroenterology, Hepatology and Nutrition, University of California, San Francisco, San Francisco, California, USA

    Elizabeth H. Yen

  2. Gastorenterology and Nutrition, The Johns Hopkins Children’s Center, Baltimore, Maryland, USA

    Amanda Radmer Leonard

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© 2015 Springer International Publishing Switzerland

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Schindler, T. (2015). Nutrition Pre and Post Lung Transplant. In: Yen, E., Leonard, A. (eds) Nutrition in Cystic Fibrosis. Nutrition and Health. Humana Press, Cham. https://doi.org/10.1007/978-3-319-16387-1_14

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  • DOI: https://doi.org/10.1007/978-3-319-16387-1_14

  • Publisher Name: Humana Press, Cham

  • Print ISBN: 978-3-319-16386-4

  • Online ISBN: 978-3-319-16387-1

  • eBook Packages: MedicineMedicine (R0)

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