Abstract
Hailey-Hailey disease (Benign familial pemphigus)
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Hailey-Hailey Disease (Benign Familial Pemphigus)
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Autosomal dominant inheritance, usually develops in the second or third decade
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Flaccid blisters and vesicles that easily rupture producing painful erosions at sites of friction on intertriginous areas (lateral neck, axilla, groin, and inframammary areas)
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Moist, malodorous vegetative plaques and fissures may develop
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Pain, pruritus, odor are the usual symptoms, and secondary bacterial infection may occur
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Acantholysis occurs in the epidermis (“dilapidated brick wall” histologically)
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Hailey-Hailey Disease (Benign Familial Pemphigus)
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A.
Flaccid blisters and vesicles that easily rupture producing painful erosions in the groin
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A.
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© 2016 Springer International Publishing Switzerland
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Gloster, H.M., Gebauer, L.E., Mistur, R.L. (2016). Hailey-Hailey Disease (Benign Familial Pemphigus). In: Absolute Dermatology Review. Springer, Cham. https://doi.org/10.1007/978-3-319-03218-4_23
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DOI: https://doi.org/10.1007/978-3-319-03218-4_23
Publisher Name: Springer, Cham
Print ISBN: 978-3-319-03217-7
Online ISBN: 978-3-319-03218-4
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