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Cleft 7

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Facial Reconstruction of Unusual Facial Clefts

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Abstract

There is a widely spread error in the medical literature, which is to name Cleft 7 all the condition in which a macrostomia is present. Some clefts 5 and all of the clefts 6 present themselves with such a symptom. In the original Tessier’s description, Cleft 7 belongs to the spectrum of hemifacial microsomia. We prefer, after McCarthy, to name this condition craniofacial microsomia. Our research reviewed 79 cases of macrostomias in the setting of craniofacial microsomia of our own patients. Depending on the series, the frequency of macrostomia in patients affected by craniofacial microsomia is around 15%. The mechanism is probably related to a defect in the fusion mechanism between the mandibular and maxillary buds of the facia primordia due to the microsomia. We discuss the technique of repair and its timing among the different stages of rehabilitation for patients with associated malformations of the mandible and external ear.

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Author information

Authors and Affiliations

  1. Plastic Surgery Department, University of Lille, Lambersart, France

    Philippe Pellerin

  2. Craniofacial Surgery Department, Universidade de São Paulo, Bauru, São Paulo, Brazil

    Cristiano Tonello

  3. Plastic Surgery Unit, Hospital de Clínicas, Universidade Federal do Paraná, Curitiba, Brazil

    Renato da Silva Freitas

  4. Craniofacial Surgery, Assistance Center for Cleft Lip and Palate (CAIF), Hospital do Trabalhador, Curitiba, Brazil

    Renato da Silva Freitas

  5. Department of Plastic Surgery, Universidade de São Paulo, São Paulo, Brazil

    Nivaldo Alonso

Authors
  1. Philippe Pellerin
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  2. Cristiano Tonello
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  3. Renato da Silva Freitas
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  4. Nivaldo Alonso
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Editor information

Editors and Affiliations

  1. Department of Plastic Surgery, Universidade de São Paulo, São Paulo, São Paulo, Brazil

    Nivaldo Alonso

  2. Plastic Surgery Unit, Hospital de Clínicas, Universidade Federal do Paraná, Curitiba, Brazil

    Renato da Silva Freitas

  3. Craniofacial Surgery Department, Universidade de São Paulo, Bauru, São Paulo, Brazil

    Cristiano Tonello

  4. Plastic Surgery Department, University of Lille, Lambersart, France

    Philippe Pellerin

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Pellerin, P., Tonello, C., da Silva Freitas, R., Alonso, N. (2023). Cleft 7. In: Alonso, N., Freitas, R.d.S., Tonello, C., Pellerin, P. (eds) Facial Reconstruction of Unusual Facial Clefts. Springer, Cham. https://doi.org/10.1007/978-3-031-40926-4_11

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  • DOI: https://doi.org/10.1007/978-3-031-40926-4_11

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-031-40925-7

  • Online ISBN: 978-3-031-40926-4

  • eBook Packages: MedicineMedicine (R0)

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