Abstract
Adult-onset Still’s disease (AOSD) may be characterized by the classic triad of persistent high spiking fever, arthralgia, and salmon-colored skin rash. AOSD may present with many different phenotypes, and it is a great mimicker of acute abdomen, heart ischemia, or sepsis. There is no specific test for the diagnosis of AOSD, but classification criteria are available. AOSD is typically considered as a diagnosis of exclusion, and a definitive diagnosis should be made based on the Yamaguchi criteria only after excluding infectious, malignant, and other connective tissue diseases. We report an interesting case of a 32-year-old male who presented right upper quadrant abdominal pain, high grade fever, and a troponin elevation. After extensive workup, potential differential diagnoses were ruled out, and the patient was diagnosed with AOSD as a diagnosis of exclusion. His course also was complicated by hemophagocytic lymphohistiocytosis (HLH).
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Zawadka, M., Mosaad, E., Wong, A. (2023). A Usual Presentation of an Unusual Case. In: Pérez-Torres, D., Martínez-Martínez, M., Schaller, S.J. (eds) Best 2022 Clinical Cases in Intensive Care Medicine. Lessons from the ICU. Springer, Cham. https://doi.org/10.1007/978-3-031-36398-6_61
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DOI: https://doi.org/10.1007/978-3-031-36398-6_61
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