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Vascular Malformations

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Pediatric Hand Surgery

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Abstract

Vascular malformations (VMs) are a complex and multifactorial conditions that can involve any area of the body for which diagnosis and treatment often require a multidisciplinary approach. VMs are congenital anomalies that are subdivided into numerous categories grouped into arterious, venous, capillary lesions or a combination of all of these. There is much confusion surrounding these little known malformations; this is due mainly to the presence of numerous and varied classifications. Misclassifications or incorrect diagnoses are common and are usually due to the limited experience of clinicians or radiologists involved in the diagnosis and management of vascular malformations; recognizing a vascular malformation and appropriately classifying it are essential for optimal patient care and require solid knowledge and experience. The origin of vascular malformations is a genetic defect that, in many associated syndromes, is inherited in an autosomal recessive manner, while in the non-inherited forms, it is a random genetic defect.

Although embolization and sclerotherapy are helpful in other districts, they should be avoided in the hand because of the high failure rate and sequela; that is why surgical treatment is the best choice for the hand.

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Author information

Authors and Affiliations

  1. Hand Surgery Unit, IRCCS Galeazzi-Sant’Ambrogio GSD, Milan, Italy

    Luciana Marzella

  2. Columbus Clinic Center, Milan, Italy

    Piero di Giuseppe

Authors
  1. Luciana Marzella
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  2. Piero di Giuseppe
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Editors and Affiliations

  1. Department of Hand Surgery and Rehabilitation, S. Giuseppe MultiMedica Hospital, Milan University, Milano, Italy

    Giorgio Pajardi

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Marzella, L., di Giuseppe, P. (2023). Vascular Malformations. In: Pajardi, G. (eds) Pediatric Hand Surgery. Springer, Cham. https://doi.org/10.1007/978-3-031-30984-7_22

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  • DOI: https://doi.org/10.1007/978-3-031-30984-7_22

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-031-30983-0

  • Online ISBN: 978-3-031-30984-7

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