Abstract
Congenital heart diseases range from diseases that can have minor symptoms and do not require treatment to diseases that pose a threat to life and need urgent surgical intervention. They are the most common among congenital diseases, which have a health, psychological, and financial burden on the infected children and their family. This chapter discusses one of these congenital heart diseases, total anomalous pulmonary venous return, which is a cardiac abnormality in which pulmonary veins are not connected right.
We have studied the latest scientific research, articles, and studies related to total anomalous pulmonary venous return, the etiology, and the types of this defect, which includes supracardiac, cardiac, infracardiac, and mixed TAPVR.
The chapter also discusses the diagnosis, signs and symptoms, pathophysiology, and the effect of this defect on the normal blood flow and normal function of the heart.
Due to recent developments and the accumulation of experiences in the field of treating congenital heart diseases, it has become possible to treat total anomalous pulmonary venous return. The concept of surgery is to create a communication between pulmonary veins and the left atrium and to close any abnormal connections. The surgical approach, risks , benefits, and complications of surgical correction are discussed in this chapter.
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References
Domadia S, et al. Neonatal outcomes in total anomalous pulmonary venous return: the role of prenatal diagnosis and pulmonary venous obstruction. Pediatr Cardiol. 2018;39(7):1346–54.
Shi X, et al. Next-generation sequencing identifies novel genes with rare variants in total anomalous pulmonary venous connection. EBioMedicine. 2018;38:217–27.
White BR, et al. Repair of total anomalous pulmonary venous connection: risk factors for postoperative obstruction. Ann Thorac Surg. 2019;108(1):122–9.
Shi G, et al. Total anomalous pulmonary venous connection: the current management strategies in a pediatric cohort of 768 patients. Circulation. 2017;135(1):48–58.
Yoshimura N, et al. Surgery for total anomalous pulmonary venous connection: primary sutureless repair vs. conventional repair. Gen Thorac Cardiovasc Surg. 2017;65(5):245–51.
Spigel ZA, et al. Total anomalous pulmonary venous connection: influence of heterotaxy and venous obstruction on outcomes. J Thorac Cardiovasc Surg. 2022;163(2):387–395.e3.
White BR, et al. Venous flow variation predicts preoperative pulmonary venous obstruction in children with Total anomalous pulmonary venous connection. J Am Soc Echocardiogr. 2021;34(7):775–85.
Jaramillo FA, et al. Infracardiac type total anomalous pulmonary venous return with obstruction and dilatation of portal vein. Radiol Case Rep. 2017;12(2):229–32.
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Al Mostafa, M. (2023). Total Anomalous Pulmonary Venous Return. In: Tagarakis, G., Gheni Sarfan, A., Hashim, H.T., Varney, J. (eds) Clinical and Surgical Aspects of Congenital Heart Diseases . Springer, Cham. https://doi.org/10.1007/978-3-031-23062-2_11
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DOI: https://doi.org/10.1007/978-3-031-23062-2_11
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