Abstract
Although being rare diseases cutaneous lymphomas, especially mycosis fungoides and Sézary syndrome, represent important differential diagnosis in dermatology that must not be overlooked. Most of the diverse cutaneous lymphomas have, in contrast to nodal lymphomas, a relatively benign clinical course, and treatment should be chosen carefully and in hindsight to this fact.
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Abbreviations
- CR:
-
Complete response
- EORTC:
-
European Organisation for Research and Treatment of Cancer
- ISCL:
-
International Society for Cutaneous Lymphomas
- OR:
-
Overall response
- ORR:
-
Overall response rate
- R-CHOP:
-
Rituximab, cyclophosphamide, hydroxydaunorubicin, vincristine, prednisolone
- R-COP:
-
Rituximab, cyclophosphamide, vincristine, prednisolone
- TCR:
-
T cell receptor gene rearrangement
Reference
Olsen E, Vonderheid E, Pimpinelli N, Willemze R, Kim Y, Knobler R, et al. Revisions to the staging and classification of mycosis fungoides and Sezary syndrome: a proposal of the International Society for Cutaneous Lymphomas (ISCL) and the cutaneous lymphoma task force of the European Organization of Research and Treatment of Cancer (EORTC). Blood. 2007;110(6):1713–22.
Senff NJ, Noordijk EM, Kim YH, Bagot M, Berti E, Cerroni L, et al. European Organization for Research and Treatment of Cancer and International Society for Cutaneous Lymphoma consensus recommendations for the management of cutaneous B-cell lymphomas. Blood. 2008b;112(5):1600–9.
Willemze R, Cerroni L, Kempf W, Berti E, Facchetti F, Swerdlow SH, et al. The 2018 update of the WHO-EORTC classification for primary cutaneous lymphomas. Blood. 2019;133(16):1703–14.
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Bauer, W., Knobler, R. (2023). Primary Cutaneous Lymphomas. In: Katsambas, A.D., Lotti, T.M., Dessinioti, C., D'Erme, A.M. (eds) European Handbook of Dermatological Treatments. Springer, Cham. https://doi.org/10.1007/978-3-031-15130-9_57
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DOI: https://doi.org/10.1007/978-3-031-15130-9_57
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