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Periocular Squamous Cell Carcinoma in a Child with Xeroderma Pigmentosum

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Part of the Clinical Cases in Dermatology book series (CLIDADE)

Abstract

Squamous cell carcinoma (SCC) is a common malignancy in adults but are exceptionally rare in children. However, children with certain disease condition, for example, xeroderma pigmentosum (XP), a rare inherited disease, is highly susceptible to the development of skin malignancy including SCC.

We report a case of XP in an 18-years old boy with clinical symptoms of lentiginous spots in the sun-exposed area, accompanied by Squamous Cell Carcinoma (SCC) in the eye based on histopathological examination.

Keywords

  • Squamous cell carcinoma
  • Malignancy
  • Xeroderma pigmentosa

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Doanh, L.H., Van Thuong, N., Tirant, M. (2022). Periocular Squamous Cell Carcinoma in a Child with Xeroderma Pigmentosum. In: Satolli, F., Tirant, M., Wollina, U., Lotti, T.M. (eds) Clinical Cases in Pediatric Skin Cancers. Clinical Cases in Dermatology. Springer, Cham. https://doi.org/10.1007/978-3-030-93666-2_27

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  • DOI: https://doi.org/10.1007/978-3-030-93666-2_27

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-93665-5

  • Online ISBN: 978-3-030-93666-2

  • eBook Packages: MedicineMedicine (R0)