Abstract
Chronic Bullous Disease of Childhood (CBDC) is a rare autoimmune disease characterized by blistering and linear deposition of IgA on the basement membrane. A frequent complication is a secondary infection of the ruptured bullous which can cause a larger wound. A case of CBDC case with hypertrophic scar complication in a 3-year-old child is reported. The diagnosis is made based on clinical, laboratory and histopathological examination. Patients responded well to dapsone treatment within 1 week of treatment, although the prognosis is poor since hypertrophic scar occurred and caused a contracture in her left knee.
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References
Nicholas MW, Rao CR, Hall RP. Linear IgA dermatosis and chronic bullous disease of childhood. In: Kang S, Amagai M, Bruckner AL, Enk AH, Margolis DJ, McMichael AJ, Orringer JS, editors. Fitzpatrick’s dermatology in general medicine. 9th ed. New York: McGraw-Hill; 2019. p. 992–1000.
Woodly DT, Chen M. Epidermolysis bullosa acquisita. In: Kang S, Amagai M, Bruckner AL, Enk AH, Margolis DJ, McMichael AJ, Orringer JS, editors. Fitzpatrick’s dermatology in general medicine. 9th ed. New York: McGraw-Hill; 2019. p. 971–9.
Weedon D. Epidermolysis bullosa acquisita. In: Skin pathology. 5th ed. Edinburgh: Churchill Livingstone; 2020. p. 177–8.
Weedon D. Linear IgA bullous dermatosis. In: Skin pathology. 5th ed. Edinburgh: Churchill Livingstone; 2020. p. 187–9.
Holahan H, Rao BK. Nonautoimmune bullous disease. In: Moschella SL, Hurley HJ, editors. Dermatology. 4th ed. Philadelphia: WB Saunders; 2020. p. 287–96.
Goh CL, Pan JY. Dapsone. In: Kang S, Amagai M, Bruckner AL, Enk AH, Margolis DJ, McMichael AJ, Orringer JS, editors. Fitzpatrick’s dermatology in general medicine. 9th ed. New York: McGraw-Hill; 2019. p. 3423–33.
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Rusyati, L.M.M., Darmaputra, I.G.N., Sudarsa, P.S.S. (2022). Chronic Bullous Disease of Childhood with Hypertrophic Scars Complications. In: Arcangeli, F., Lotti, T.M. (eds) Clinical Cases in Early-Years Pediatric Dermatology. Clinical Cases in Dermatology. Springer, Cham. https://doi.org/10.1007/978-3-030-89089-6_11
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DOI: https://doi.org/10.1007/978-3-030-89089-6_11
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