Abstract
Congenital ossicular chain abnormalities behind normal ear canal and tympanic membrane are much rarer when compared to conductive hearing loss (CHL) caused by acquired causes. They usually fail neonatal hearing screening tests. It can be diagnosed early if air and bone conduction ABR is done. They usually present as non-progressive hearing loss since birth. If there is an additional sensorineural hearing loss component, they usually present with poor language development. It is seen in cochlear hypoplasia cases. Conductive component is usually due to oval window atresia or stapes footplate fixation. This brings the concept of performing stapedotomy in cases with IEMs. In this chapter, radiological, audiological features, and stapedotomy option in cochlear hypoplasia are presented with case presentations.
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References
Sennaroglu L. Histopathology of inner ear malformations: do we have enough evidence to explain pathophysiology? Cochlear Implants Int. 2016;17(1):3–20.
Donaldson JA, Lambert PM, Duckert LG, Rubel EW. Surgical anatomy of the temporal bone. New York: Raven Press; 1992.
Sennaroglu L, et al. Manubrio-stapedioplasty: new surgical technique for malleus and incus fixation due to tympanosclerosis. J Laryngol Otol. 2015;129(6):587–90.
Sennaroglu L, et al. Oval window atresia: a novel surgical approach and pathognomonic radiological finding. Int J Pediatr Otorhinolaryngol. 2014;78(5):769–76.
Sennaroglu L. Cochlear implantation in inner ear malformations—a review article. Cochlear Implants Int. 2010;11(1):4–41.
Sennaroglu L, Bajin MD. Classification and current management of inner ear malformations. Balkan Med J. 2017;34(5):397–411.
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Sennaroglu, L., Bajin, M.D., Cinar, B.C. (2022). Stapedotomy. In: Sennaroglu, L. (eds) Inner Ear Malformations. Springer, Cham. https://doi.org/10.1007/978-3-030-83674-0_14
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DOI: https://doi.org/10.1007/978-3-030-83674-0_14
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