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Vasculitides Including IgA Vasculitis (Henoch–Schönlein Purpura)

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Textbook of Pediatric Gastroenterology, Hepatology and Nutrition

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Abstract

Inflammation of the blood vessels (vasculitis) is uncommon in childhood with the exception of IgA vasculitis (Henoch–Schönlein purpura) and Kawasaki’s disease. The disease can be classified according to the size of blood vessel affected. The gastrointestinal (GI) clinical manifestations vary according to the size and type of blood vessel involved but include GI bleeding, gastrointestinal ulceration, GI obstruction, GI perforation, and abdominal pain. Nonspecific mucosal inflammation might also be present. Diagnosis is often delayed because the presentation is so varied. Diagnostic evaluation may include GI panendoscopy, videocapsule endoscopy, abdominal ultrasound, and/or MRI and visceral angiography. Treatment is disease and presentation specific.

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Authors and Affiliations

  1. Division of Neurogastroenterology and Motility, Department of Gastroenterology, Great Ormond Street Hospital for Children NHS Foundation Trust, London, UK

    Karunesh Kumar & Keith J. Lindley

  2. Division of Intestinal Rehabilitation and Nutrition, Department of Gastroenterology, Great Ormond Street Hospital for Children NHS Foundation Trust, London, UK

    Karunesh Kumar & Jutta Köglmeier

Authors
  1. Karunesh Kumar
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  2. Jutta Köglmeier
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  3. Keith J. Lindley
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Correspondence to Keith J. Lindley .

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Editors and Affiliations

  1. Section of Pediatric Gastroenterology Hepatology and Nutrition, University of Chicago, Chicago, IL, USA

    Stefano Guandalini

  2. Pediatric Liver, GI and Nutrition Center, Child Health, King’s College Hospital, London, UK

    Anil Dhawan

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Kumar, K., Köglmeier, J., Lindley, K.J. (2022). Vasculitides Including IgA Vasculitis (Henoch–Schönlein Purpura). In: Guandalini, S., Dhawan, A. (eds) Textbook of Pediatric Gastroenterology, Hepatology and Nutrition. Springer, Cham. https://doi.org/10.1007/978-3-030-80068-0_32

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  • DOI: https://doi.org/10.1007/978-3-030-80068-0_32

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