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Abstract

Patients with severe chest wall deformity have a decreased capacity of the respiratory muscles due to rib cage deformity that can cause chronic respiratory failure. In recent years, NIMV treatment has become popular in patients with chronic respiratory failure due to chest-wall deformity. NIMV treatment can improve quality of sleep, physical activity, and quality of life.

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Abbreviations

FBN1:

Fibrillin-1

KS:

Kyphoscoliosis

MFS:

Marfan syndrome

NIMV:

Noninvasive mechanical ventilation

NIPPV:

Noninvasive positive-pressure ventilation

NIV:

Noninvasive ventilation

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Orhon Ergün, M., Zengin, S.U. (2021). Chest Wall Disorders. In: Esquinas, A.M. (eds) Pulmonary Function Measurement in Noninvasive Ventilatory Support. Springer, Cham. https://doi.org/10.1007/978-3-030-76197-4_15

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  • DOI: https://doi.org/10.1007/978-3-030-76197-4_15

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-76196-7

  • Online ISBN: 978-3-030-76197-4

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