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Double-Outlet Right Ventricle

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Pediatric Cardiac CT in Congenital Heart Disease

Abstract

Double-outlet right ventricle (DORV) accounts for 1–3% of all congenital heart defects. The diagnosis of DORV is generally made by two-dimensional echocardiography. However, given the shortcomings in transthoracic echocardiography to delineate the extent of ventricular septal defect and great artery relationship and coronary arteries in young infants, cardiac CT is increasingly used both in preoperative and postoperative evaluation of DORV. The common indications for cardiac CT in DORV patients include evaluation of the pathway for ventricular septal defect closure and coronary arteries. The preferred cardiac CT technique is prospective gated cardiac CT using modern dual-source multidetector CT scanners; however retrospective gated CT is commonly used for ventricular volume evaluation.

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Correspondence to Dilachew A. Adebo .

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Schoeneberg, L., Adebo, D.A. (2021). Double-Outlet Right Ventricle. In: Adebo, D.A. (eds) Pediatric Cardiac CT in Congenital Heart Disease. Springer, Cham. https://doi.org/10.1007/978-3-030-74822-7_17

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  • DOI: https://doi.org/10.1007/978-3-030-74822-7_17

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  • Publisher Name: Springer, Cham

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  • Online ISBN: 978-3-030-74822-7

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