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Biphenotypic Sinonasal Sarcoma

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Soft Tissue Tumors

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Abstract

Biphenotypic sinonasal sarcoma is a malignant tumor recently recognized by the World Health Organization.

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Notes

  1. 1.

    PAX3 (paired box 3) encodes a member of the paired box transcription factor family (which plays a critical role in fetal development). PAX3 rearrangements are found also in alveolar rhabdomyosarcoma

  2. 2.

    MAML3 (Mastermind Like Transcriptional Coactivator 3) encodes a protein with transcription coactivator activity

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  • Jo (2018) Expression of PAX3 Distinguishes Biphenotypic Sinonasal Sarcoma From Histologic Mimics. Am J Surg Pathol 42(10):1275–1285

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  • Wang (2014) Recurrent PAX3-MAML3 fusion in biphenotypic sinonasal sarcoma. Nat Genet 46:666–668

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Authors and Affiliations

  1. Department of Surgery Oncology and Gastroenterology, University of Padova, Padova, Italy

    Simone Mocellin

  2. Melanoma and Soft Tissue Sarcoma Unit, Istituto Oncologico Veneto (IOV-IRCCS) of Padova, Padova, Italy

    Simone Mocellin

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  1. Simone Mocellin
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Correspondence to Simone Mocellin .

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Mocellin, S. (2021). Biphenotypic Sinonasal Sarcoma. In: Soft Tissue Tumors . Springer, Cham. https://doi.org/10.1007/978-3-030-58710-9_37

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  • DOI: https://doi.org/10.1007/978-3-030-58710-9_37

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-58709-3

  • Online ISBN: 978-3-030-58710-9

  • eBook Packages: MedicineMedicine (R0)

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