Abstract
Particularly in endemic regions, parenchymal neuro-Behçet syndrome (p-NBS) should be considered in the differential diagnosis when patients are admitted with chronic and progressive gait disturbances. As there are no other biomarkers for NBS, magnetic resonance imaging (MRI) remains the gold standard in the differential diagnosis of p-NBS as well as in predicting prognosis and treatment response. The most commonly confused disease with p-NBS is multiple sclerosis. One of the main clinical differences between p-NBS and MS is that patients with the relapsing form of MS usually recover well, while those with the relapsing form of p-NBS do not. The other difference between MS and NBS relies on different MRI patterns and cerebrospinal fluid findings.
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Uygunoglu, U., Siva, A. (2021). Neuro-Behçet Syndrome: Differential Diagnosis. In: Tüzün, E., Kürtüncü, M. (eds) Neuro-Behçet’s Disease. Springer, Cham. https://doi.org/10.1007/978-3-030-55273-2_7
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