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Congenital Upper Tract Anomalies: Duplication, Cystic Renal Dysplasia, Multicystic Dysplastic Kidney

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Practical Pediatric Urology

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Abstract

Congenital anomalies of the kidneys or lower urinary tract (CAKUT) are the most common causes of renal failure in children and lead to approximately 25% of end-stage renal disease in adults. Amongst the spectrum of anomalies includes renal duplication, cystic renal dysplasia, and Multicystic Dyplastic Kidney (MCDK). Developmental defects leading to these entities can occur in isolation or as part of a syndromic pattern. This chapter provides a practical overview of the diagnosis, pathophysiology, and management options for the common and most clinically significant congenital upper tract anomalies.

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Author information

Authors and Affiliations

  1. Department of Urology, Maine Medical Center, S. Portland, ME, USA

    David Chalmers

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  1. David Chalmers
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Correspondence to David Chalmers .

Editor information

Editors and Affiliations

  1. Department of Paediatric Surgery, Sheffield Children’s Foundation Trust, Sheffield, UK

    Prasad Godbole

  2. Division of Urology, University of Colorado Division of Urology, Aurora, CO, USA

    Duncan T. Wilcox

  3. Department of Surgery and IHPME, University of Toronto Paediatric Urology, The Hospital for Sick Children, Toronto, ON, Canada

    Martin A. Koyle

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Chalmers, D. (2021). Congenital Upper Tract Anomalies: Duplication, Cystic Renal Dysplasia, Multicystic Dysplastic Kidney. In: Godbole, P., Wilcox, D.T., Koyle, M.A. (eds) Practical Pediatric Urology. Springer, Cham. https://doi.org/10.1007/978-3-030-54020-3_10

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  • DOI: https://doi.org/10.1007/978-3-030-54020-3_10

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-54019-7

  • Online ISBN: 978-3-030-54020-3

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