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Early Repolarization Syndrome

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Electrocardiography of Inherited Arrhythmias and Cardiomyopathies

Abstract

Early repolarization syndrome (ERS) is a rare cardiac condition characterized by J-point elevation (JPE) on the ECG and an increased risk of sudden cardiac death due to polymorphic ventricular tachycardia or ventricular fibrillation. Because of the high prevalence of JPE in the general population, the diagnosis of ERS in presymptomatic patients and the subsequent implementation of primary prevention strategies (e.g., implantable cardioverter-defibrillator insertion) are extremely challenging. In the past decade, electrocardiographic markers for increased risk in individuals with JPE have been investigated in an attempt to improve risk stratification strategies. This chapter focuses on how to diagnose ERS and identify ECG markers of increased arrhythmic risk. Consensus statements and recommendations for the management of these patients will also be discussed.

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Author information

Authors and Affiliations

  1. Department of Cardiology, Toronto General Hospital and the University of Toronto, Toronto, ON, Canada

    Arnon Adler

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  1. Arnon Adler
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Correspondence to Arnon Adler .

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Editors and Affiliations

  1. Department of Medicine, University of Ottawa, Ottawa, ON, Canada

    Martin Green

  2. Department of Medicine, University of British Columbia, Vancouver, BC, Canada

    Andrew Krahn

  3. Department of Medicine, University of Ottawa, Ottawa, ON, Canada

    Wael Alqarawi

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Adler, A. (2020). Early Repolarization Syndrome. In: Green, M., Krahn, A., Alqarawi, W. (eds) Electrocardiography of Inherited Arrhythmias and Cardiomyopathies. Springer, Cham. https://doi.org/10.1007/978-3-030-52173-8_4

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  • DOI: https://doi.org/10.1007/978-3-030-52173-8_4

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-030-52172-1

  • Online ISBN: 978-3-030-52173-8

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