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Cystic Fibrosis

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Clinical Handbook of Psychological Consultation in Pediatric Medical Settings

Part of the book series: Issues in Clinical Child Psychology ((ICCP))

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Abstract

Cystic fibrosis (CF) is a life-shortening genetic disease that results in the overproduction of thick, sticky mucus throughout the body. Symptoms are progressive, and management requires a burdensome daily medical regimen. Individuals with CF also require hospital admissions lasting 10–14 days to treat illness exacerbations. Given that individuals with CF and their caregivers are more likely to develop symptoms of anxiety and depression, inpatient CL providers are in a prime position to deliver psychological treatment to children and families while also interfacing with and educating the medical team (both inpatient and outpatient). Common referral concerns can include, but are not limited to, anxiety and depression, adherence promotion, coping with disease progression, and promoting function in the hospital environment. Working effectively with bedside staff and attending medical providers are a key focus of treatment for individuals with CF and their families. Aspects of interventions should be modified as appropriate for this population, particularly keeping in mind infection control guidelines.

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Author information

Authors and Affiliations

  1. Cincinnati Children’s Hospital Medical Center, Cincinnati, OH, USA

    Adrienne P. Borschuk & Stephanie S. Filigno

  2. Behavioral Medicine and Clinical Psychology, Cincinnati Children’s Hospital Medical Center, Cincinnati, OH, USA

    Adrienne P. Borschuk & Stephanie S. Filigno

  3. University of Cincinnati College of Medicine, Cincinnati, OH, USA

    Adrienne P. Borschuk & Stephanie S. Filigno

Authors
  1. Adrienne P. Borschuk
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  2. Stephanie S. Filigno
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Corresponding author

Correspondence to Stephanie S. Filigno .

Editor information

Editors and Affiliations

  1. Pediatric Consultation-Liaison Service, Norton Children’s Hospital, Louisville, KY, USA

    Bryan D. Carter

  2. Department of Pediatrics, University of Louisville, School of Medicine, Louisville, KY, USA

    Bryan D. Carter

  3. Department of Pediatrics, C.S. Mott Children’s Hospital Michigan Medicine, Ann Arbor, MI, USA

    Kristin A. Kullgren

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Borschuk, A.P., Filigno, S.S. (2020). Cystic Fibrosis. In: Carter, B.D., Kullgren, K.A. (eds) Clinical Handbook of Psychological Consultation in Pediatric Medical Settings. Issues in Clinical Child Psychology. Springer, Cham. https://doi.org/10.1007/978-3-030-35598-2_25

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