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Genetics of Idiopathic Pulmonary Fibrosis

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Part of the book series: Respiratory Medicine ((RM))

Abstract

In the last two decades, there has been significant growth in our understanding of the genetics underlying idiopathic pulmonary fibrosis (IPF), a relentlessly progressive, incurable disease. Where once the pathogenesis of IPF remained a mystery, modern methods in genetics and genetic epidemiology have begun to point investigators toward a better understanding of why this disease occurs and also toward more personalized approaches to patient care via the identification of new potential therapeutic targets for IPF.

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Acknowledgments

The authors would like to thank Dr. Raphael Borie, Dr. Christopher J.G. Sigakis, Mr. Avram Walts, Dr. Yasushi Nakano, and Dr. Evgenia Dobrinskikh for their assistance in preparing figures for this manuscript.

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Mathai, S.K., Schwartz, D.A. (2020). Genetics of Idiopathic Pulmonary Fibrosis. In: Gomez, J., Himes, B., Kaminski, N. (eds) Precision in Pulmonary, Critical Care, and Sleep Medicine. Respiratory Medicine. Humana, Cham. https://doi.org/10.1007/978-3-030-31507-8_6

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