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Macular Dystrophies

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Handbook of Clinical Electrophysiology of Vision

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Abstract

This chapter summarizes the application of electroretinogram and/or electrooculogram in patients with Stargardt’s disease, fundus flavimaculatus, X-linked retinoschisis, vitelliform macular dystrophy (Best’s disease), pattern dystrophies, macular pattern dystrophy, Doyne’s honeycomb macular dystrophy, occult macular dystrophy, and North Carolina macular dystrophy.

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Author information

Authors and Affiliations

  1. Center for Retinal Degenerations and Ophthalmic Genetic Diseases, Duke University School of Medicine, Duke Eye Center, Department of Ophthalmology, Durham, NC, USA

    Wajiha Jurdi Kheir, Alfonso Senatore, Roberto Gattegna, Alessandro Racioppi & Alessandro Iannaccone

  2. Department of Ophthalmology, University Hospitals Eye Institute, Cleveland, OH, USA

    Minzhong Yu

  3. Retina Service, Israelitic Hospital, Rome, Italy

    Roberto Gattegna

  4. University of North Carolina, Chapel Hill, NC, USA

    Alessandro Racioppi

  5. Moran Eye Center, University of Utah School of Medicine, Salt Lake City, UT, USA

    Donnell Creel

Authors
  1. Wajiha Jurdi Kheir
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  2. Minzhong Yu
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  3. Alfonso Senatore
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  4. Roberto Gattegna
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  5. Alessandro Racioppi
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  6. Donnell Creel
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  7. Alessandro Iannaccone
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Corresponding author

Correspondence to Minzhong Yu .

Editor information

Editors and Affiliations

  1. Department of Ophthalmology, University Hospitals Eye Institute, Cleveland, OH, USA

    Minzhong Yu

  2. Moran Eye Center, University of Utah School of Medicine, Salt Lake City, UT, USA

    Donnell Creel

  3. Center for Retinal Degenerations and Ophthalmic Genetic Diseases, Duke University School of Medicine, Duke Eye Center, Department of Ophthalmology, Durham, NC, USA

    Alessandro Iannaccone

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Kheir, W.J. et al. (2019). Macular Dystrophies. In: Yu, M., Creel, D., Iannaccone, A. (eds) Handbook of Clinical Electrophysiology of Vision. Springer, Cham. https://doi.org/10.1007/978-3-030-30417-1_5

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