Abstract
Large-vessel pulmonary artery sarcomas are rare tumors of the pulmonary vasculature, accounting for only a fraction of primary lung cancers and with a very poor prognosis. They arise proximally from within the pulmonary artery and spread within the arterial lumen, causing obstruction of the vasculature that may result in right ventricular failure. Although they may have a similar presentation to chronic thromboembolic pulmonary disease and CTEPH, there are subtle indicators in history and imaging that can help with their differential diagnosis, with the confirmation usually resulting from tissue biopsy. This case presentation focuses on this CTEPH mimic.
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Papamatheakis, D.G., Gopalan, D., Auger, W.R. (2020). Case 9: Pulmonary Artery Sarcoma Mimicking Massive Thromboembolic Disease. In: Auger, W., Gopalan, D. (eds) Clinical Cases in Chronic Thromboembolic Pulmonary Hypertension. Clinical Cases in Cardiology. Springer, Cham. https://doi.org/10.1007/978-3-030-17366-1_9
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DOI: https://doi.org/10.1007/978-3-030-17366-1_9
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