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Lymphangioleiomyomatosis

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Transbronchial cryobiopsy in diffuse parenchymal lung disease

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Abstract

Pulmonary lymphangioleiomyomatosis (LAM) is a rare disease that almost exclusively occurs in women of childbearing age, most often appearing as a diffuse cystic lung disease due to proliferations of distinctive smooth-muscle cell-like cells along lymphatic channels progressively involving the pulmonary parenchyma and the pleura [1–3].

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Author information

Authors and Affiliations

  1. Operative Unit of Pathologic Anatomy, Hospital St. Maria delle Croci, Azienda USL della Romagna, Ravenna, Italy

    Giulio Rossi

  2. Operative Unit of Pathologic Anatomy, Hospital “Degli Infermi”, Azienda USL della Romagna, Rimini, Italy

    Mirca Valli

  3. Department of Pathology, Operative Unit of Pathologic Anatomy, Azienda USL della Romagna, Ospedale GB Morgagni-L Pierantoni, Forlì, Italy

    Alessandra Dubini

  4. Section of Respiratory Diseases, Department of Cardiac, Thoracic and Vascular Sciences, University of Padova, Padova, Italy

    Paolo Spagnolo

Authors
  1. Giulio Rossi
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  2. Mirca Valli
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  3. Alessandra Dubini
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  4. Paolo Spagnolo
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Corresponding author

Correspondence to Giulio Rossi .

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Editors and Affiliations

  1. Department of Diseases of the Thorax, Ospedale Morgagni-Pierantoni, Forlì, Italy

    Venerino Poletti

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Rossi, G., Valli, M., Dubini, A., Spagnolo, P. (2019). Lymphangioleiomyomatosis. In: Poletti, V. (eds) Transbronchial cryobiopsy in diffuse parenchymal lung disease. Springer, Cham. https://doi.org/10.1007/978-3-030-14891-1_14

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  • DOI: https://doi.org/10.1007/978-3-030-14891-1_14

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