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Non-compaction ventriculaire gauche : rôles et potentialités de l’imagerie dans le diagnostic d’une forme frontière d’une maladie myocardique

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Résumé

L’augmentation considérable du nombre de publications concernant le ventricule gauche non compacté (VGNC) témoigne de l’intérêt grandissant de la communauté internationale pour cette entité particulière du myocarde. Ce VGNC est caractérisé par la présence de trabéculations proéminentes et de récessus intratrabéculaires profonds [1]. La paroi myocardique est dans cette entité constituée d’une couche fine de muscle compacté associée à une couche épaisse de muscle sous-endocardique trabéculé. Il existe cependant toujours des discussions pour savoir si cette entité est une réelle cardiomyopathie bien individualisée ou s’il s’agit d’une expression phénotypique partagée entre plusieurs cardiomyopathies distinctes. Cette anomalie peut être effectivement présente de façon isolée ou associée à diverses cardiopathies (anomalies congénitales simples telle que la maladie d’Ebstein ou complexes cardiopathies hypertrophiques et/ou dilatées).

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Mousseaux, E., Macron, L. (2013). Non-compaction ventriculaire gauche : rôles et potentialités de l’imagerie dans le diagnostic d’une forme frontière d’une maladie myocardique. In: Boyer, L., Guéret, P. (eds) Imagerie en coupes du cœur et des vaisseaux. Springer, Paris. https://doi.org/10.1007/978-2-8178-0435-4_15

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  • DOI: https://doi.org/10.1007/978-2-8178-0435-4_15

  • Publisher Name: Springer, Paris

  • Print ISBN: 978-2-8178-0434-7

  • Online ISBN: 978-2-8178-0435-4

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