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Épidémiologie des cancers de l’enfant pp 213–216Cite as

Maladie des exostoses multiples

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Abstrait

La maladie des exostoses multiples (MEM) est caractérisée cliniquement par la présence d’exostoses ou ostéochondromes (tumeurs bénignes) se développant principalement au niveau des métaphyses des os longs. Le risque de dégénérescence en chondrosarcome à l’âge adulte est estimé à 5%.

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Authors and Affiliations

  1. INSERM U781, Département de génétique Hôpital Necker-Enfants Malades, 149, rue de Sèvres, 75743, Paris Cedex 15

    Laurence Legeai-Mallet

  2. Département de génétique Hôpital Necker-Enfants Malades, Université Paris Descartes INSERM U781, 149, rue de Sèvres, 75743, Paris Cedex 15

    Valérie Cormier-Daire

Authors
  1. Laurence Legeai-Mallet
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  2. Valérie Cormier-Daire
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© 2009 Springer-Verlag France

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Legeai-Mallet, L., Cormier-Daire, V. (2009). Maladie des exostoses multiples. In: Épidémiologie des cancers de l’enfant. Springer, Paris. https://doi.org/10.1007/978-2-287-78337-1_24

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  • DOI: https://doi.org/10.1007/978-2-287-78337-1_24

  • Publisher Name: Springer, Paris

  • Print ISBN: 978-2-287-78336-4

  • Online ISBN: 978-2-287-78337-1

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