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Manifestations dermatologiques des maladies du système hématopoïétique et oncologie dermatologique pp 226–257Cite as

Génodermatoses prédisposant aux cancers

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Abstrait

Les génodermatoses prédisposant aux cancers constituent un large groupe d’affections dermatologiques ou àprésentation dermatologique souvent rares, qui sont associées avec une fréquence élevée àla survenue de tumeurs malignes cutanées et/ou viscérales. À l’exception de la neurofibromatose de type 1 et de la sclérose tubéreuse de Bourneville, elles sont peu ou mal connues, ce qui a pour conséquence un retard diagnostique préjudiciable àla prévention et au dépistage des éventuelles néoplasies associées 1-3. Pourtant le mode d’entrée de ces génodermatoses peut se diagnostiquer dans bon nombre de cas lors d’une consultation de dermatologie. C’est le cas, par exemple, des léiomyomes de la léiomyomatose familiale cutanée, des fïbrofolliculomes du syndrome de Birt-Hogg-Dubé, des hamartomes multiples de la maladie de Cowden, de la lentiginose du syndrome de Peutz-Jeghers et du complexe de Carney, de la leucokératose et de l’onychopathie de la dyskératose de Zinsser-Cole-Engman ou de la canitie et du vieillissement cutané prématuré du syndrome de Werner.

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Authors and Affiliations

  1. Service de Dermatologie, Hôpital Saint-Éloi, 80 avenue Augustin-Fliche, 34295, Montpellier CEDEX 5

    Didierer Bessis & Nicolas Kluger

  2. Service de Dermatologie, Hôpital Caremeau, Place du Professeur-Debré, 30029, Nîmes

    Myriam Marque

  3. Service de Génétique médicale, Hôpital Arnaud-de-Villeneuve, 80 avenue Augustin-Fliche, 34295, Montpellier CEDEX 5

    Isabelle Coupier

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  1. Didierer Bessis
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  4. Isabelle Coupier
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Bessis, D., Marque, M., Kluger, N., Coupier, I. (2009). Génodermatoses prédisposant aux cancers. In: Manifestations dermatologiques des maladies du système hématopoïétique et oncologie dermatologique. Springer, Paris. https://doi.org/10.1007/978-2-287-72092-5_20

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  • DOI: https://doi.org/10.1007/978-2-287-72092-5_20

  • Publisher Name: Springer, Paris

  • Print ISBN: 978-2-287-72091-8

  • Online ISBN: 978-2-287-72092-5

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