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Pancréas

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Tumeurs malignes rares

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Résumé

Les tumeurs rares du pancréas sont mieux connues depuis une décennie. Les progrès de l’imagerie ont contribué à leur reconnaissance. Le diagnostic est un enjeu important pour la stratégie thérapeutique, en particulier pour certaines lésions kystiques bénignes qui, lorsqu’elles sont reconnues avec certitude, peuvent être surveillées (1, 2). Nous avons retenu pour cette étude, le pancréatoblastome, tumeur la plus fréquente de l’enfant, dont le diagnostic différentiel principal chez l’enfant et l’adolescente est la tumeur pseudo-papillaire et solide (TPS). Seules les tumeurs kystiques épithéliales et non épithéliales seront envisagées; les kystes vrais ne seront pas envisagés (kystes épithéliaux non tumoraux comme le lymphangiome kystique ou le kyste para-ampullaire de la paroi duodénale plus connu sous le nom de dystrophie kystique du pancréas) de même que les kystes observés dans le cadre des polykystoses hépatorénales (il s’agit de pseudo-tumeurs).

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  1. Département de chirurgie viscérale oncologique, Institut Paoli-Calmettes, 13-15, Boulevard de Sainte-Marguerite, 13009, Marseille

    Jean-Robert Delpero

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Delpero, JR. (2010). Pancréas. In: Tumeurs malignes rares. Springer, Paris. https://doi.org/10.1007/978-2-287-72070-3_81

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  • DOI: https://doi.org/10.1007/978-2-287-72070-3_81

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