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Ebstein’s Disease

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Critical Care of Children with Heart Disease

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Abstract

Ebstein’s disease is a congenital cardiac anomaly that occurs with an incidence of approximately 1–5 in every 20,000 live newborns, therefore representing 1% of congenital cardiac defects. It is the most common etiology for congenital tricuspid regurgitation in the neonatal period as well as later in life. The etiology of Ebstein’s anomaly is unknown, however, a number of environmental factors have been implicated, namely maternal exposure to varnishing substances and maternal use of benzodiazepines and lithium ingestion during the first trimester of pregnancy.

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Authors and Affiliations

  1. Pediatric Cardiology and Cardiac Intensive Care, Department of Pediatrics, The Children’s Hospital of Denver, Aurora, CO, USA

    Eduardo M. da Cruz

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  1. Eduardo M. da Cruz
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  2. Jonathan Kaufman
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  3. Victor O. Morell
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Correspondence to Eduardo M. da Cruz .

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Editors and Affiliations

  1. Children's Hospital, Pittsburgh, 5th Ave. 3705, Pittsburgh, 15213, USA

    Ricardo Munoz

  2. School of Medicine, Children's Hospital, University of Pittsburgh, Fifth Ave. 3705, Pittsburgh, 15213, USA

    Victor Morell

  3. Chemin de Normanie 2, Geneve, 1206, Switzerland

    Eduardo Cruz

  4. Children's Hospital, Pittsburgh, 5th Ave. 3705, Pittsburgh, 15213, USA

    Carol Vetterly

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© 2009 Springer-Verlag London Limited

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da Cruz, E.M. et al. (2009). Ebstein’s Disease. In: Munoz, R., Morell, V., Cruz, E., Vetterly, C. (eds) Critical Care of Children with Heart Disease. Springer, London. https://doi.org/10.1007/978-1-84882-262-7_37

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  • DOI: https://doi.org/10.1007/978-1-84882-262-7_37

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-84882-261-0

  • Online ISBN: 978-1-84882-262-7

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