Abstract
Pulmonic stenosis refers to an obstruction at or distal to the right ventricular outflow. Owing to various possible levels of obstruction, this disease is not a homogeneous entity. Obstruction can be found at the valvar level, the right ventricular (RV) infundibulum, and/or the supravalvular level within the main pulmonary artery or distal to it at multiple levels. It is also found in association with ventricular septal defect and overriding aorta as in Tetralogy of Fallot (TOF) (see associated chapter). In patients suffering from congenital heart disease, 25–30% suffer from some form of pulmonary stenosis [1].
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Domnina, Y.A., Muñoz, R., Kreutzer, J., Morell, V.O. (2009). Pulmonary Stenosis. In: Munoz, R., Morell, V., Cruz, E., Vetterly, C. (eds) Critical Care of Children with Heart Disease. Springer, London. https://doi.org/10.1007/978-1-84882-262-7_23
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