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The Differential Diagnosis of Inflammatory Myopathy

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The Inflammatory Myopathies

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Abstract

The differential diagnosis of idiopathic inflammatory myopathy is broad, encompassing a variety of disorders affecting the motor unit. Primary muscle disorders that must be considered include congenital myopathy, hereditary metabolic disorders, and muscular dystrophy. Secondary muscle disorders include those associated with collagen vascular disease or malignancy or due to infection, drugs, or toxins. Disorders of the neuromuscular junction, such as myasthenia gravis, and anterior horn cell disease may also present as proximal muscle weakness.

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Acknowledgment

We would like to thank Salvatore DiMauro for reviewing portions of the transcript and for helpful comments and suggestions.

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  1. Department of Neurology, Division of Neuromuscular Disease, Weill Cornell Medical College, New York, NY, USA

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    Rubin, M., Klein, A. (2009). The Differential Diagnosis of Inflammatory Myopathy. In: Kagen, L. (eds) The Inflammatory Myopathies. Humana Press. https://doi.org/10.1007/978-1-60327-827-0_14

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