Familial Adult-Onset Spinocerebellar Degenerations

  • James H. Bower
Part of the Current Clinical Practice book series (CCP)


The familial spinocerebellar degenerations are a heterogeneous group of disorders with onset in both childhood and adulthood. Their prevalence is estimated to be between 1.5 and 22.1 per 100,000. Although pathologic and clinical classification systems have been proposed in the past, all have had shortcomings. In the past several years, great strides in genetics have radically changed our thinking about the classification, and thus clinical presentation, of these disorders. In this chapter, we concentrate on the adult-onset familial ataxias.


Multiple System Atrophy Spinocerebellar Ataxia Spinocerebellar Ataxia Type Familial Hemiplegic Migraine Episodic Ataxia 
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Selected Reading

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Copyright information

© Springer Science+Business Media New York 2000

Authors and Affiliations

  • James H. Bower

There are no affiliations available

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