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The Pathogenesis of Duchenne Muscular Dystrophy

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Pathogenesis of Neurodegenerative Disorders

Part of the book series: Contemporary Neuroscience ((CNEURO))

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Abstract

Duchenne muscular dystrophy (DMD) is a lethal X-linked inherited muscle-wasting disease (Duchenne, 1868; Gowers, 1879; Emery, 1993). It is the most common genetic neuromuscular disease, with an estimated incidence of 1 in 3500 live male births (Emery, 1993).

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Authors
  1. Edward A. Burton
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  2. Kay E. Davies
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Editors and Affiliations

  1. Laboratory of Neurosciences, National Institute on Aging, Baltimore, MD, USA

    Mark P. Mattson

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Burton, E.A., Davies, K.E. (2001). The Pathogenesis of Duchenne Muscular Dystrophy. In: Mattson, M.P. (eds) Pathogenesis of Neurodegenerative Disorders. Contemporary Neuroscience. Humana Press, Totowa, NJ. https://doi.org/10.1007/978-1-59259-106-0_12

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  • DOI: https://doi.org/10.1007/978-1-59259-106-0_12

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