Sudden Cardiac Death in the Young

  • Christopher B. Stefanelli
  • Aarti DalalEmail author
  • Robert Campbell


Sudden cardiac death (SCD) in the young tends to occur in individuals with undiagnosed heart disease and has a devastating impact on families and communities. Such events tend to draw substantial public and media attention, particularly when a young athlete is involved. Heightened awareness of SCD has led to anxiety regarding youth athletics as well as debate regarding appropriate and cost-effective screening. It is important to note that many pediatric, nonathletic cardiopulmonary arrests are either of a respiratory or traumatic etiology. Nonetheless, sudden cardiac arrest (SCA) is the leading cause of death in young athletes and may be preventable in many cases. However, current screening methods in the USA are inadequate to identify those at risk with sufficient sensitivity or specificity, or in a practical or cost-effective manner.


Arrhythmogenic right ventricular cardiomyopathy (ARVC) Brugada syndrome Catecholaminergic polymorphic ventricular tachycardia (CPVT) Channelopathies Commotio cordis Congenital abnormalities of the coronary arteries Fontan operation Hypertrophic cardiomyopathy (HCM) Left heart obstructive lesions Myocarditis Prevention of sudden cardiac death Primary prevention Pulmonary hypertension Secondary prevention Sudden cardiac death (SCD) Sudden infant death syndrome Tetralogy of Fallot Transposition of the great arteries Wolff–Parkinson–White syndrome 

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Copyright information

© Springer Science+Business Media, New York 2015

Authors and Affiliations

  • Christopher B. Stefanelli
    • 1
  • Aarti Dalal
    • 2
    Email author
  • Robert Campbell
    • 2
  1. 1.Department of Pediatric CardiologyHawaii Permanente Medical GroupHonoluluUSA
  2. 2.Sibley Heart Center, Children’s Healthcare of Atlanta, Department of PediatricsEmory University School of MedicineAtlantaUSA

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