Clinical Presentation and Diagnostic Considerations

  • Audra A. DuncanEmail author


The syndrome of celiac artery compression by the median arcuate ligament (MAL) or possibly by fibrotic celiac ganglion was first described by Harjola in 1963 and then by Dumbar et al. in 1965. Symptoms may vary from postprandial abdominal pain, similar to that seen with chronic mesenteric ischemia, to pain with exercise, nausea, vomiting, or weight loss. Diagnosis may be confounded by a vague and variable clinical presentation, as well as by the fact that celiac compression by the ganglion is a normal variant noted on imaging in asymptomatic patients. In fact, extrinsic compression of the celiac artery may be found in 20–70 % of individuals undergoing imaging for possible abdominal disease.


Median arcuate ligament syndrome Celiac artery compression syndrome Fibrotic celiac ganglion compression Diagnosis of medical arcuate ligament syndrome Compression of the celiac trunk 


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Copyright information

© Springer Science+Business Media New York 2015

Authors and Affiliations

  1. 1.Division of Vascular and Endovascular Surgery, Department of SurgeryMayo ClinicRochesterUSA

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