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Lesions of Anogenital Mammary-Like Glands, Adnexal Neoplasms, and Metastases

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Vulvar Pathology

Abstract

The vulva contains a high density of apocrine and anogenital mammary-like glands relative to eccrine glands and pilosebaceous units; therefore, the spectrum of glandular neoplasms reflects the relative frequency of these structures. Commonly encountered benign and malignant lesions include hidradenoma papilliferum and syringoma; and extramammary Paget’s disease, respectively. Rarer lesions of anogenital mammary-like glands such as hidradenoma papilliferum, fibroadenoma, phyllodes tumor, and carcinomas of anogenital mammary-like glands can present as diagnostic challenge. To this list, adnexal tumors as seen in other part of the body like hidradenoma, sebaceoma, poroma, cylindroma, spiradenoma, and chondroid syringoma should be included in the differential diagnosis of a mass in the vulva.

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Hoang, M.P., Kazakov, D.V. (2015). Lesions of Anogenital Mammary-Like Glands, Adnexal Neoplasms, and Metastases. In: Hoang, M., Selim, M. (eds) Vulvar Pathology. Springer, New York, NY. https://doi.org/10.1007/978-1-4939-1807-2_11

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