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Muscular dystrophies

  • Michael Swash
  • Martin S. Schwartz
Part of the Biopsy Pathology Series book series (BPS)

Abstract

The muscular dystrophies are relatively uncommon inherited disorders of muscle. They are characterized by a progressive course and by degenerative changes in skeletal muscle fibres. Most begin in childhood but in others the disease is not recognized until adult life. Classification depends on clinical, genetic and histological criteria (Table 6.1). The childhood myopathies are, by convention, classified separately since these disorders are only very slowly progressive and they show only mild myopathic changes in the muscle, although there may be particular features in certain of these disorders.

Keywords

Muscular Dystrophy Duchenne Dystrophy Muscle Spindle Duchenne Muscular Dystrophy Myotonic Dystrophy 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© M. Swash and M. S. Schwartz 1984

Authors and Affiliations

  • Michael Swash
    • 1
    • 2
  • Martin S. Schwartz
    • 3
  1. 1.The London Hospital and St Mark’s HospitalLondonUK
  2. 2.Senior Lecturer in NeuropathologyThe London Hospital Medical CollegeLondonUK
  3. 3.St George’ Hospital (Atkinson Morley’s Hospital)LondonUK

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