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Wegener’s Granulomatosis and Henoch-Schönlein Purpura in a Family with Hereditary C4 Deficiency

  • K. Lhotta
  • F. Kronenberg
  • M. Joannidis
  • H. Feichtinger
  • P. König
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 336)

Summary

Described here is a family in which the father with partial C4 deficiency had Wegener’s granulomatosis and a son with complete C4 deficiency presented with Henoch-Schönlein Purpura. The possible role of C4 deficiency in the pathogenesis of both vasculitic disorders is discussed.

Keywords

Crescentic Glomerulonephritis Alternative Complement Pathway Vasculitic Disorder SchOnlein Purpura 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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References

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Copyright information

© Springer Science+Business Media New York 1993

Authors and Affiliations

  • K. Lhotta
    • 1
  • F. Kronenberg
    • 1
  • M. Joannidis
    • 1
  • H. Feichtinger
    • 2
  • P. König
    • 1
  1. 1.Dept. of Internal MedicineInnsbruck University HospitalInnsbruckAustria
  2. 2.Institute of PathologyInnsbruck University HospitalInnsbruckAustria

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