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Transient Hyperammonemias in Infants with and without Organic Acidemia

  • W. L. Nyhan
  • V. Rubio
  • A. Jordá
  • S. Grisolia
  • F. Gutierez
  • C. Canosa
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 153)

Abstract

Transient hyperammonemia of the newborn was first described in 1978 in 5 preterm infants1. During that period this disorder appeared in our experience to be the most common form of symptomatic neonatal hyperammonemia. More recently, we have not studied a patient with this disorder in more than 2 years, while the number of patients referred to us for diagnosis of hyperammonemia has increased. Whether these observations reflect a real changing incidence of the disorder remains to be determined.

Keywords

Urea Cycle Glutaric Aciduria Type Ornithine Transcarbamylase Propionic Acidemia Methylmalonic Acidemia 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Science+Business Media New York 1982

Authors and Affiliations

  • W. L. Nyhan
    • 1
    • 2
  • V. Rubio
    • 1
    • 2
  • A. Jordá
    • 1
    • 2
  • S. Grisolia
    • 1
    • 2
  • F. Gutierez
    • 1
    • 2
  • C. Canosa
    • 1
    • 2
  1. 1.University of California San DiegoLa JollaUSA
  2. 2.Instituto de Investigaciones CitologicasValencia Spain, and Hospital Infantil La FeValenciaSpain

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