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Biochemical Studies on Brain Explants and Fibroblast Cultures in Batten’s Disease

  • John H. Menkes
  • Don R. Harris
  • Natalie Stein
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 19)

Abstract

Batten’s disease is a syndrome of mental, motor, and visual deterioration having its onset between the second and fifth year of life. Through combined ultrastructural and biochemical examinations at least five different entities are currently known to assume a clinical course corresponding to that described by Batten in 1914 (1).

Keywords

Linoleic Acid Stearic Acid Fatty Acid Ester Fibroblast Culture Label Fatty Acid 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Science+Business Media New York 1972

Authors and Affiliations

  • John H. Menkes
    • 1
  • Don R. Harris
    • 1
  • Natalie Stein
    • 1
  1. 1.Division of Pediatric NeurologyUniversity of California at Los Angeles and Brentwood V.A. HospitalUSA

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