Biochemical Studies on Brain Explants and Fibroblast Cultures in Batten’s Disease
Batten’s disease is a syndrome of mental, motor, and visual deterioration having its onset between the second and fifth year of life. Through combined ultrastructural and biochemical examinations at least five different entities are currently known to assume a clinical course corresponding to that described by Batten in 1914 (1).
KeywordsLinoleic Acid Stearic Acid Fatty Acid Ester Fibroblast Culture Label Fatty Acid
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