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Tetralogy of Fallot

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Part of the book series: Comprehensive Manuals of Surgical Specialties ((CMSS))

Abstract

It is now a quarter century since total correction of tetralogy of Fallot was first reported by Lillehei41 and demonstrated to be a feasible, low-risk operation by Kirklin.33 During that time significant advances have occurred. Such advances, however, have not completely resolved the continuing controversy over when surgical intervention is indicated and what surgical approach should be taken-the two-stage approach of a palliative procedure to increase pulmonary blood flow followed by later total correction or the one-stage approach of primary total correction. Whatever approach is taken, surgery has an extremely important role in tetralogy of Fallot. The life expectancy without surgery is extremely poor: one-third of patients will die before 1 year. half before 3 years, and only one-quarter will live to 10 years.6

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References

  1. Adams P, Radley-Smith R, Yacoub M: Primary total correction of Fallot’s tetralogy below the age of 2 years. Br Heart J 36: 1036, 1974.

    PubMed  CAS  Google Scholar 

  2. Alfieri O, Locatelli G, Bianchi T, Vanini V, Parenzan L: Repair of tetralogy of Fallot after Waterston anastomosis. J Thorac Cardiovasc Surg 77: 826, 1979.

    PubMed  CAS  Google Scholar 

  3. Arciniegas E, Farooki ZQ, Hakimi M, Green EW: Results of two-stage surgical treatment of tetralogy of Fallot. J Thorac Cardiovasc Surg 79: 876, 1980.

    PubMed  CAS  Google Scholar 

  4. Barratt-Boyes BG, Neutze JM: Primary repair of tetralogy of Fallot in infancy using profound hypothermia with circulatory arrest and limited cardiopulmonary bypass: a comparison with conventional two stage management. Ann Surg 178: 406, 1973.

    Article  PubMed  CAS  Google Scholar 

  5. Berry BE, McGoon DC: Total correction for tetralogy of Fallot with anomalous coronary artery. Surgery 74: 894, 1973.

    PubMed  CAS  Google Scholar 

  6. Bertranou EG, Blackstone EH, Hazelrig JB, Turner ME Jr, Kirklin JW: Life expectancy without surgery in tetralogy of Fallot. Am J Cardiol 41: 458, 1978.

    Article  Google Scholar 

  7. Blackstone EH, Kirklin JW, Bertranou EG, Labrosse CJ, Soto B, Bargeron LM: Preoperative prediction from cineangiograms of post-repair right ventricular pressure in tetralogy of Fallot. J Thorac Cardiovasc Surg 78: 542, 1979.

    PubMed  CAS  Google Scholar 

  8. Blackstone EH, Kirklin JW, Pacifico AD: Decision-making in repair of tetralogy of Fallot based on intraoperative measurements of pulmonary arterial outflow tract. J Thorac Cardiovasc Surg 77: 526, 1979.

    PubMed  CAS  Google Scholar 

  9. Blalock A: Discussion of Lillehei et al: Direct vision intracardiac surgical correcTetralogy of Fallottion of the tetralogy of Fallot, pentalogy of Fallot and pulmonary atresia defects. Ann Surg 142: 418, 1955.

    Article  Google Scholar 

  10. Bonchek LI, Starr A, Sunderland CO, Menashe VD: Natural history of tetralogy of Fallot in infancy: clinical classification and therapeutic implications. Circulation 48: 392, 1973.

    Article  PubMed  CAS  Google Scholar 

  11. Bristow JD, Kloster FE, Lees MH, Menashe VD, Griswold HE, Starr A: Serial cardiac catheterizations and exercise hemodynamics after correction of tetralogy of Fallot. Average follow-up 13 months and 7 years after operation. Circulation 41: 1057, 1970.

    Article  PubMed  CAS  Google Scholar 

  12. Burnell RH, Woodson RD, Lees MH, Bristow JD, Starr A: Results of correction of tetralogy of Fallot in children under four years of age. J Thorac Cardiovasc Surg 57: 153, 1969.

    PubMed  CAS  Google Scholar 

  13. Calder AL, Barratt-•Boyer BG, Brandt PWT, Neutze JM: Postoperative evaluation of patients with tetralogy of Fallot repaired in infancy. Including criteria for use of outflow patching and radiologie assessment of pulmonary regurgitation. J Thorac Cardiovasc Surg 77: 704, 1979.

    PubMed  CAS  Google Scholar 

  14. Castaneda AR, Freed MD, Williams RG, Norwood WI: Repair of tetralogy of Fallot in infancy. J Thorac Cardiovasc Surg 74: 372, 1977.

    PubMed  CAS  Google Scholar 

  15. Castaneda AR, Sade RM, Lamberti J, Nicoloff DM: Reoperation for residual defects after repair of tetralogy of Fallot. Surgery 76: 1010, 1974.

    PubMed  CAS  Google Scholar 

  16. Cumming GR: Propranolol in tetralogy of Fallot. Editorial. Circulation 41: 13, 1970.

    Article  CAS  Google Scholar 

  17. Dabizzi RP, Caprioli G, Aiazzi L, Castelli C, Baldrighi G, Parenzan I., Baldrighi V: Distribution and anomalies of coronary arteries in tetralogy of Fallot. Circulation 61: 95, 1980.

    Article  PubMed  CAS  Google Scholar 

  18. Daily PO, Stinson EB, Griepp RB, Shumway NE: Tetralogy of Fallot: choice of surgical procedure. J Thorac Cardiovasc Surg 7: 338. 1978.

    Google Scholar 

  19. Edmunds LH Jr, Saxena NC, Friedman S, Rashkind JW, Dodd PF: Transatrial repair of tetralogy of.Fallot. Surgery 80: 681, 1976.

    PubMed  Google Scholar 

  20. Fallot A: Contribution of l’anatomie pathologique de la maladie bleue (cyanose cardiaque). Marseille Med 25:77, 138, 207, 270. 341, 403, 1888.

    Google Scholar 

  21. Fallot A: Contribution to the pathologic anatomy of morhus caeruleus (translated summary). In Willins, Keys (eds): Cardiac Classic.. St Louis, CV Mosby Co. 1941, pp 689, 690.

    Google Scholar 

  22. Gale AW, Arciniegas E, Green EW, Blackstone EH, Kirklin JW: Growth of the pulmonary anulus and pulmonary arteries after the Blalock-Taussig shunt. J Thorac Cardiovasc Surg 77: 459, 1979.

    PubMed  CAS  Google Scholar 

  23. Garson A Jr, Gorry GA, McNamara DG, Cooley DA: The surgical decision in tetralogy of Fallot: weighing risks and benefits with decision analysis. Am J Cardiol 45: 108, 1980.

    Article  PubMed  Google Scholar 

  24. Garson A, Nihill MR, McNamara DG, Cooley DA: Status of the adult and adolescent after repair of tetralogy of Fallot. Circulation 59: 1232, 1979.

    Article  PubMed  Google Scholar 

  25. Gay WA Jr, Ebert PA: Aorta-to-right pulmonary artery anastomosis causing obstruction of the right pulmonary artery management during correction of tetralogy of Fallot. Ann Thorac Surg 16: 402, 1973.

    Article  PubMed  Google Scholar 

  26. Gill GC. Moodie DS, McGeon DC: Staged surgical management of pulmonary atresia with diminutive pulmonary arteries. J Thorac Cardiovasc Surg 73: 436, 1977

    PubMed  CAS  Google Scholar 

  27. Gillette PC, Garson A, Eterovic F., Nehces W, Mullins CE, McNamara DG: Results of oral propranolol in infants and children. J Pediatr 86: 170, 1978.

    Google Scholar 

  28. Gillette PC, Yeoman MA, Mullins CE, McNamara DG: Sudden death after repair of tetralogy of Fallot. electrocardiographic and electrophysiologic abnormal-nies. Circulation 56: 566, 1977.

    Article  PubMed  CAS  Google Scholar 

  29. Howe A, Rastelli GC, Ritter DG, DuShane JW, MVlcGoon DC: Management of the right ventricular outflow tract in severe tetralogy of Fallot. J Thorac Cardiovasc Surg 60: 131, 1970.

    Google Scholar 

  30. Jones EL, Conti CR, Neill CA, Gott VL, Brawley RK, Haller JA: Long-term evaluation of tetralogy patients with pulmonary valvular insufficiency resulting from outflow-patch correction across the pulmonic annulus. Circulation 48 (Suppl III): III - 11, 1973.

    Google Scholar 

  31. Kirklin JW, Blackstone EH, Pacifico AD, Brown RN, Bargeron LM: Routine primary repair vs two-stage repair of tetralogy of Fallot. Circulation 60: 373, 1979.

    Article  PubMed  CAS  Google Scholar 

  32. Kirklin JW, Devloo RA: Hypothermic perfusion and circulatory arrest for surgical correction of tetralogy of Fallot with previously constructed Potts’ anastomosis. Dis Chest 39: 87, 1961.

    Article  PubMed  CAS  Google Scholar 

  33. Kirklin JW, Ellis FH, McGoon DC, DuShane JW, Swan JC: Surgical treatment for the tetralogy of Fallot by open intracardiac repair. J Thorac Cardiovasc Surg 37: 22, 1959.

    CAS  Google Scholar 

  34. Kirklin JW, Payne WS: Surgical treatment for tetralogy of Fallot after previous anastomosis of systemic to pulmonary artery. Surg Gynecol Obstet 110: 707, 1960.

    PubMed  CAS  Google Scholar 

  35. Kirklin JW, Wallace RB, McGoon DC, DuShane JW: Early and late results after intracardiac repair of tetralogy of Fallot. Ann Surg 162: 578, 1965.

    Article  PubMed  CAS  Google Scholar 

  36. Krongard E: Prognosis for patients with congenital heart disease and postoperative intraventricular conduction defects. Circulation 57: 867, 1978.

    Article  Google Scholar 

  37. Lakier JB, Stanger P, Heymann MA, Hoffman JIE, Rudolph AM: Tetralogy of Fallot with absent pulmonary valve. Natural history and hemodynamic considerations. Circulation 50: 167, 1974.

    Article  PubMed  CAS  Google Scholar 

  38. Lev M: The architecture of the conduction system in congenital heart disease. II. Tetralogy of Fallot. Arch Pathol Lab Med 67: 572, 1959.

    CAS  Google Scholar 

  39. Lev M: Conduction system in congenital heart disease. Am J Cardiol 21: 619, 1968.

    Article  PubMed  CAS  Google Scholar 

  40. Lev M, Eckner RAO: The pathologic anatomy of tetralogy of Fallot and its variations. Dis Chest 45: 251, 1964.

    Article  PubMed  CAS  Google Scholar 

  41. Lillehei CW, Cohen M, Warden HE, Reed RC, Aust JB, Dewall RA, Varco RL: Direct vision intracardiac surgical correction of the tetralogy of Fallot, pentalogy of Fallot and pulmonary atresia defects. Ann Surg 142: 418, 1955.

    Article  PubMed  CAS  Google Scholar 

  42. Litwin SB, Rosenthal A, Fellows K: Surgical management of young infants with tetralogy of Fallot, absence of the pulmonary valve, and respiratory distress. J Thorac Cardiovasc Surg 65: 552, 1973.

    PubMed  CAS  Google Scholar 

  43. McGoon DC: Discussion of Pacifico et al: Surgical management of pulmonary stenosis in tetralogy of Fallot. J Thorac Cardiovasc Surg 74: 382, 1977.

    Google Scholar 

  44. Meyer J, Chiarello L, Hallman GL, Cooley DA: Coronary artery anomalies in patients with tetralogy of Fallot. J Thorac Cardiovasc Surg 69: 373, 1975.

    PubMed  CAS  Google Scholar 

  45. Miller RA, Lev M, Paul MH: Congenital absence of the pulmonary valve: the clinical syndrome of tetralogy of Fallot with pulmonary regurgitation. Circulation 26: 266, 1962.

    Article  PubMed  CAS  Google Scholar 

  46. Mistrot JJ, Bernhard WF, Rosenthal A, Castaneda AR: Tetralogy of Fallot with a single pulmonary artery: operative repair. Ann Thorac Surg 23: 249, 1977.

    Article  PubMed  CAS  Google Scholar 

  47. Norwood WI, Rosenthal A, Castaneda AR: Tetralogy of Fallot with acquired pulmonary atresia and hypoplasia of pulmonary arteries. J Thorac Cardiovasc Surg 72: 454, 1976.

    PubMed  CAS  Google Scholar 

  48. Oku H, Shirotani H, Yokoyama T, Tokota Y, Kawai J, Mori A, Kanzaki Y, Makino S, Ando F, Setsuie N: Postoperative size of the right ventricular outflow tract and optimal age in complete repair of tetralogy of Fallot. Ann Thorac Surg 25: 322, 1978.

    Article  PubMed  CAS  Google Scholar 

  49. Pacifico AD, Bargeron LM, Kirklin JW: Primary total correction of tetralogy of Fallot in children less than four years of age. Circulation 48: 1085, 1973.

    Article  PubMed  CAS  Google Scholar 

  50. Pacifico AD, Kirklin JW, Blackstone EH: Surgical management of pulmonary stenosis in tetralogy of Fallot. J Thorac Cardiovasc Surg 74: 382, 1977.

    PubMed  CAS  Google Scholar 

  51. Poirer RA, McGoon DC, Danielson GK, Wallace RB, Ritter DG, Moodie DS, Wiltse CG: Late results after repair of tetralogy of Fallot. J Thorac Cardiovasc Surg 73: 900, 1977.

    Google Scholar 

  52. Puga FJ, DuShane JW, McGoon DC: Treatment of tetralogy of Fallot in children less than 4 years of age. J Thorac Cardiovasc Surg 64: 247, 1972.

    PubMed  CAS  Google Scholar 

  53. Rees GM, Starr A: Total correction of Fallot’s tetralogy in patients aged less than 1 year. Br Heart J 35: 898, 1973.

    Article  PubMed  CAS  Google Scholar 

  54. Rocchini AP, Rosenthal A, Freed M, Castaneda AR, Nadas AS: Chronic congestive heart failure after repair of tetralogy of Fallot. Circulation 56: 305, 1977.

    Article  PubMed  CAS  Google Scholar 

  55. Rosing DR, Borer JS, Kent KM, Maron BJ, Seides SF, Morrow AG, Epstein SE: Long-term hemodynamic and electrocardiographic assessment following operative repair of tetralogy of Fallot. Circulation 58 (Su.ppl III): III - 209, 1978.

    Google Scholar 

  56. Rowlatt UF, Rimoldi HJA, Lev M: The quantitative anatomy of the normal child’s heart. Pediatr Clin North Am 10: 499, 1963.

    Google Scholar 

  57. Stafford EG, Mair DD, McGoon DC, Danielson GK: Tetralogy of Fallot with absent pulmonary valve. Circulation 48 (Suppl III): III - 24, 1973.

    Google Scholar 

  58. Starr A, Bonchek LI, Sunderland CO: Total correction of tetralogy of Fallot in infancy. J Thorac Cardiovasc Surg 65: 45, 1973.

    PubMed  CAS  Google Scholar 

  59. Steeg CN, Krongrad E, Davachi F, Bowman FO Jr, Malm JR, Gersony WM: Postoperative left anterior hemiblock and right bundle branch block following repair of tetralogy of Fallot. Circulation 51: 1026, 1975.

    Article  PubMed  CAS  Google Scholar 

  60. Stephenson LW, Friedman S, Edmunds LH: Staged surgical management of tetralogy of Fallot in infants. Circulation 58: 837, 1978.

    Article  PubMed  CAS  Google Scholar 

  61. Sunderland CO, Matarazzo RG, Lees MH, Menashe VD, Bonchek LI, Rosenberg JA, Starr A: Total correction of tetralogy of Fallot: postoperative hemodynamic evaluation. Circulation 48: 398, 1973.

    Article  PubMed  CAS  Google Scholar 

  62. Tucker WY, Turley K, Ullyot DJ, Ebert PA: Management of symptomatic tetralogy of Fallot in the first year of life. J Thorac Cardiovasc Surg 78: 494, 1979.

    PubMed  CAS  Google Scholar 

  63. Turley K, Tucker WY, Ebert PA: The changing role of palliative procedures in the treatment of infants with congenital heart disease. J Thorac Cardiovasc Surg 79: 194, 1980.

    PubMed  CAS  Google Scholar 

  64. Venugopal P, Subramanian S: Intracardiac repair of tetralogy of Fallot in patients under five years of age. Ann Thorac Surg 18: 228, 1974.

    Article  PubMed  CAS  Google Scholar 

  65. Wolff GS, Rowland TW, Ellison RC: Surgically induced right bundle-branch block with left anterior hemiblock: an ominous sign in postoperative tetralogy of Fallot. Circulation 46: 587, 1972.

    Article  PubMed  CAS  Google Scholar 

  66. Yabek SM, Jarmakani JM, Roberts NK: Diagnosis of trifascicular damage following tetralogy of Fallot and ventricular septal defect repair. Circulation 55: 23, 1977.

    Article  PubMed  CAS  Google Scholar 

  67. Zavanella C, Matsuda H, Subramanian S: Successful correction of a complete form of atrioventricular canal associated with tetralogy of Fallot. J Thorac Cardiovasc Surg 74: 195, 1977.

    PubMed  CAS  Google Scholar 

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Harlan, B.J., Starr, A., Harwin, F.M. (1981). Tetralogy of Fallot. In: Manual of Cardiac Surgery. Comprehensive Manuals of Surgical Specialties. Springer, New York, NY. https://doi.org/10.1007/978-1-4757-4118-6_9

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  • DOI: https://doi.org/10.1007/978-1-4757-4118-6_9

  • Publisher Name: Springer, New York, NY

  • Print ISBN: 978-1-4757-4120-9

  • Online ISBN: 978-1-4757-4118-6

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