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Family Medicine pp 1006-1016 | Cite as

Selected Disorders of the Blood and Hematopoietic System

  • Paul M. Paulman
  • Nancy Wolf-Gillespie
  • Layne A. Prest

Abstract

Hemophilia A is an autosomal recessive X-linked deficiency of factor VIII. Because of the mode of transmission and gene expression, males have hemophilia A, and females are usually asymptomatic carriers of the hemophilia A gene. All daughters of a hemophiliac father are carriers of the hemophilia A gene; all his sons are normal. The children of a female hemophilia A carrier have a 50% chance of being affected by the gene. Hemophilia A affects approximately 1 in 10,000 to 20,000 males in the United States.1

Keywords

Sickle Cell Anemia Factor Viii Sickle Cell Disseminate Intravascular Coagulation Disseminate Intravascular Coagulation 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Science+Business Media New York 1994

Authors and Affiliations

  • Paul M. Paulman
  • Nancy Wolf-Gillespie
  • Layne A. Prest

There are no affiliations available

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