Periodic Plasma Exchanges in the Treatment of Familial Amyloid Polyneuropathy: Preliminary Results
TTRMet 30 interferes directly with the nerve fiber metabolism and its function.
The decrease of the normal TTR (TTRVal 30) is responsible for nerve fiber degeneration.
The presence of amyloid causes the neuropathy (but definitely not by a mechanical or vascular effect, as postulated before, otherwise it would correspond to a mononeuropathy multiplex and not to a generalized polyneuropathy).
KeywordsAutonomic Neuropathy Neurological Score Familial Amyloid Polyneuropathy Familial Amyloidotic Polyneuropathy Partial Score
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