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An Autopsy Case of Recessive Dystrophic Epidermolysis Bullosa Complicating Secondary Systemic Amyloidosis

  • Shigehiro Yi
  • Yoshihiro Kimura
  • Kiyoshi Takahashi
  • Komyo Eto
  • Reiko Nogami
  • Yoshihiro Maekawa
  • Tatsuyoshi Arao
  • Shukuro Araki
Chapter

Abstract

Recessive dystrophic epidermolysis bullosa (RDEB) is a hereditary disorder characterized by the development from birth of bullae or erosions on the skin accompanied by chronic inflammation. Recently, we had an opportunity to examine an autopsy case of RDEB complicated with systemic secondary amyloidosis.

Keywords

Amyloid Deposit Epidermolysis Bullosa Systemic Amyloidosis Hypochromic Anemia Secondary Amyloidosis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer Science+Business Media New York 1988

Authors and Affiliations

  • Shigehiro Yi
    • 1
    • 3
  • Yoshihiro Kimura
    • 1
    • 3
  • Kiyoshi Takahashi
    • 1
  • Komyo Eto
    • 1
  • Reiko Nogami
    • 2
  • Yoshihiro Maekawa
    • 2
  • Tatsuyoshi Arao
    • 2
  • Shukuro Araki
    • 3
  1. 1.Second Department of PathologyKumamoto University Medical SchoolKumamoto 860Japan
  2. 2.Department of DermatologyKumamoto University Medical SchoolKumamoto 860Japan
  3. 3.First Department of Internal MedicineKumamoto University Medical SchoolKumamoto 860Japan

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