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Renal Involvement in Tuberous Sclerosis

  • F. Dossi
  • A. M. Marconi
  • P. Riegler
  • M. Broggini
  • D. Donati
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 252)

Abstract

Tuberous Sclerosis (T.S.) is an autosomal dominant inherited disease with high penetrance but variable expressivity. According to recent studies the gene for T.S. is on the distal long arm of chromosome 9.1 Criteria for diagnosis have been established and include clinical and radiological criteria.2,3

Keywords

Chronic Renal Failure Tuberous Sclerosis Renal Involvement Renal Cyst Acute Pyelonephritis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Plenum Press, New York 1989

Authors and Affiliations

  • F. Dossi
    • 1
  • A. M. Marconi
    • 2
  • P. Riegler
    • 3
  • M. Broggini
    • 4
  • D. Donati
    • 1
  1. 1.Dept. of NephrologyGeneral HospitalVareseItaly
  2. 2.Dept. of UrologyGeneral HospitalVareseItaly
  3. 3.Dept. of Internal MedicineGeneral HospitalVareseItaly
  4. 4.Dept. of NephrologyGeneral HospitalBolzanoItaly

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