The Therapeutic Possibilities in the Hemoglobinopathies
In recent years there has been a rapid increase in knowledge about the structure and function of the hemoglobin molecule in health and disease. Many genetic disorders of hemoglobin synthesis have been described and the molecular basis of the associated clinical pictures elucidated. Unfortunately none of these advances have led to an improvement in the clinical management of affected patients.
KeywordsExchange Transfusion Globin Chain Hypochromic Anemia Hemoglobin Molecule Total Deficiency
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