Sialidase in Brain and Fibroblasts in Three Patients with Different Types of Sialidosis

  • Bernhard Pallmann
  • Konrad Sandhoff
  • Bruno Berra
  • Tadashi Miyatake
Part of the Advances in Experimental Medicine and Biology book series (AEMB, volume 125)


In recent years numerous diseases have become known which are characterized by an elevated urinary excretion of sialooligosaccharides and a deficiency of sialidase in cultured fibroblasts (for literature, see SPRANGER, GEHLER and CANTZ, 1977; STRECKER and MICHALSKI, 1978; MAROTEAUX, 1978).


Sialic Acid Lysosomal Enzyme Postmortem Brain Lysosomal Storage Disease Sialic Acid Content 
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Copyright information

© Plenum Press, New York 1980

Authors and Affiliations

  • Bernhard Pallmann
    • 1
  • Konrad Sandhoff
    • 1
  • Bruno Berra
    • 2
  • Tadashi Miyatake
    • 3
  1. 1.Neurochemische AbteilungMax-Planck-Institut für PsychiatrieMünchen 40Germany
  2. 2.College of PharmacyUniversity of MilanItaly
  3. 3.Department of NeurologyJichi Medical SchoolYakushiji, TochigiJapan

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